OCCURRENCE OF URINARY ACID MUCOPOLYSACCHARIDES IN THE HURLER SYNDROME
نویسندگان
چکیده
منابع مشابه
The occurrence of acid mucopolysaccharides in human leukocytes and urine.
Acid mucopolysaccharides have been found in urine (1) but have not been consistently demonstrated in the blood of normal subjects. Bassiouni (2) recently isolated a substance from leukocytes which he noted to be similar to chondroitin sulfate. In our laboratory leukocytes have been found to contain appreciable quantities of a substance resembling chondroitin sulfate. A direct relationship betwe...
متن کاملTHE HURLER SYNDROME TABLE II Intracellular Mucopolysaccharides in Cztltured Lymphoid and Skin Fibroblast Lines Derived from a Patient with the Hurler Syndrome
The Hurler syndrome is a genetic disorder in mucopolysaccharide metabolism which results in storage of mucopolysaccharides in various tissues of the body (1). The lymphocytes in the peripheral blood of patients with the Hurler syndrome show metachromatic inclusions which are considered to be diagnostic (2). I t has not been established whether these inclusions reflect the uptake of mucopolysacc...
متن کاملDecrease of urinary acid mucopolysaccharides in Hurler's syndrome after plasma infusion.
ORII, T., YAMAGUCHI, M., MINAMI, R. and NAKAO, T. Decrease of Urinary Acid Mueopolysaccharides in Hurler's Syndrome after Plasma Infusion. Tohoku J. exp. Med., 1974, 112 (4), 385-387 The fresh plasma infusion in patients affected by Hurler, Scheie or Morquio syndromes was followed by a decreased urinary excretion of chondroitin sulfate B or keratosulfate. Furthermore, in all of the patients the...
متن کاملUrinary Excretion of Acid Mucopolysaccharides by Patients with Rheumatoid Arthritis'
Several methods have been described for the determination of urinary acid mucopolysaccharides (1-4). It has been found that in normal individuals the daily urinary excretion varies with age and sex (4, 5). A few attempts have been made to correlate urinary excretion of acid mucopolysaccharides with different disease states. Craddock and Kerby (6) have reported that patients with impairment of r...
متن کاملUrinary excretion of acid mucopolysaccharides by patients with rheumatoid arthritis.
Several methods have been described for the determination of urinary acid mucopolysaccharides (1-4). It has been found that in normal individuals the daily urinary excretion varies with age and sex (4, 5). A few attempts have been made to correlate urinary excretion of acid mucopolysaccharides with different disease states. Craddock and Kerby (6) have reported that patients with impairment of r...
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ژورنال
عنوان ژورنال: Proceedings of the National Academy of Sciences
سال: 1957
ISSN: 0027-8424,1091-6490
DOI: 10.1073/pnas.43.6.443